Registre pour suivre l’issue du traitement et la pratique médicale de l'hypertension pulmonaire pendant l'enfance

Inclusion Criteria:

- Patient must be an incident patient, i.e.newly diagnosed with PH

- Age at time of diagnosis is at least 3 months and less than 18 years

- Patients must present with PH belonging to one of the following categories

- Group 1 according to updated Nice clinical classification

- Group 3 according to updated Nice clinical classification

- Group 4 according to updated Nice clinical classification

- Group 5 according to updated Nice clinical classification

- PH confirmed by heart catheterisation (HC)

- At HC, the patient must present with mean pulmonary arterial pressure (PAP) of at
least 25 mmHg at rest, a pulmonary vascular resistance index (PVRi) equal to or below
3 Wood units*m^2 and mean pulmonary arterial wedge pressure (PAWP) below or equal to
15 mmHg

- In case of congenital heart disease (CHD) patients who had undergone palliative
procedure or repair to close systemic to pulmonary shunt, the diagnosis of PH must
have been confirmed by HC at least 6 months after surgery/palliative procedure took
place

- For patients with PAH-CHD open shunt, only those considered not operable due to
advanced pulmonary vascular disease are eligible

- Patients to be included into the registry, and/or their legal guardians, must give
informed consent. Where applicable patients will be asked for their written assent

- Participating sites must agree to adhere to the recommendations of the WSPH 2015 Nice,
Pediatric Taskforce.

Exclusion Criteria:

- Patients belonging to Group 2 according to updated Nice clinical classification